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1.
Rev. esp. investig. quir ; 21(1): 13-15, 2018. ilus
Artigo em Espanhol | IBECS | ID: ibc-173357

RESUMO

El síndrome de Herlyn-Werner-Wünderlich (HWW) constituye una rara anomalía congénita mülleriana caracterizada por la aso-ciación de útero didelfo, septum vaginal y agenesia renal homolateral. Presentamos el caso de una paciente de 48 años de edadremitida por dismenorrea y que finalmente es diagnosticada de éste síndrome. Durante el examen físico se visualiza fondo de sacoen cara lateral izquierda de la vagina, lo que sería compatible con una vagina rudimentaria. La resonancia magnética confirmaeste hallazgo y muestra un útero didelfo bicollix así como agenesia renal izquierda. Debido a la edad de la paciente y a la ausenciade deseo genésico se realiza histerectomía total con doble anexectomía


Herlyn-Werner-Wünderlich syndrome (HWW) is a rare Mullerian congenital abnormality. This syndrome is characterized by the association between didelphis uterus, obstructive vaginal septum, and homolateral renal agenesis. We report the case of a 48-year old female who was diagnosed with this syndrome in the context of dysmenorrhea and pelvic pain. During physical examination, an orifice on the left lateral aspect of the vagina was visualized and it was compatible with a rudimentary vagina. Magnetic resonance confirmed this finding and showed a didelphis uterus and left renal agenesis. Due to the age of the patient and the absence of gestational desire, a total hysterectomy with double-annexectomy was performed


Assuntos
Humanos , Feminino , Pessoa de Meia-Idade , Dismenorreia/complicações , Síndrome de Werner/diagnóstico por imagem , Síndrome de Werner/cirurgia , Histerectomia/métodos , Vagina/diagnóstico por imagem , Seroma/complicações , Procedimentos Cirúrgicos Urogenitais/métodos , Seroma/diagnóstico por imagem , Anormalidades Urogenitais/diagnóstico por imagem , Anormalidades Urogenitais/cirurgia , Vagina/cirurgia , Diagnóstico Precoce
4.
Actas Urol Esp ; 30(1): 85-9, 2006 Jan.
Artigo em Espanhol | MEDLINE | ID: mdl-16703736

RESUMO

OBJECTIVE: We report a case of Ovarian Vein Syndrome, describe its clinical symptoms and discuss its diagnosis and management including laparoscopic surgery treatment. MATERIALS AND METHODS: A 36-year-old female with right kidney recurring pain was studied by means of abdominal RX, urography, CT, MRI and ultrasonography and finally diagnosed from Ovarian Vein Syndrome. The case was resolved with laparoscopic surgery. CONCLUSIONS: Ovarian Vein Syndrome is an uncommon disorder. Differential diagnosis must be done with external processes that cause ureteral obstruction. Surgery is the first line treatment when clinical symptoms are present and, in our opinion,laparoscopic surgery is the best approach to treat this pathology.


Assuntos
Laparoscopia , Ovário/irrigação sanguínea , Doenças Vasculares/cirurgia , Adulto , Feminino , Humanos , Síndrome
5.
Actas urol. esp ; 30(1): 85-89, ene. 2006. ilus
Artigo em Es | IBECS | ID: ibc-043241

RESUMO

Objetivo: Presentamos un caso de síndrome de la vena ovárica, describimos su presentación clínica y discutimos su diagnóstico y tratamiento incluyendo la cirugía laparoscópica. Material y Métodos: Mujer de 36 años de edad con clínica de cólico renal derecho recurrente que tras ser estudiada mediante radiología de abdomen, urografías, TAC, RM y ecografía es diagnosticada finalmente de síndrome de la vena ovárica. El caso se resuelve con cirugía laparoscópica. Conclusiones: El síndrome de la vena ovárica es una entidad poco frecuente. El diagnóstico diferencial se debe hacer con procesos extrínsecos que producen obstrucción ureteral. El tratamiento es quirúrgico cuando produce síntomas y pensamos que actualmente debe hacerse por vía laparoscópica


Objective: We report a case of Ovarian Vein Syndrome, describe its clinical symptoms and discuss its diagnosis and management including laparoscopic surgery treatment. Materials and Methods: A 36-year-old female with right kidney recurring pain was studied by means of abdominal RX, urography, CT, MRI and ultrasonography and finally diagnosed from Ovarian Vein Syndrome. The case was resolved with laparoscopic surgery. Conclusions: Ovarian Vein Syndrome is an uncommon disorder. Differential diagnosis must be done with external processes that cause ureteral obstruction. Surgery is the first line treatment when clinical symptoms are present and, in our opinion, laparoscopic surgery is the best approach to treat this pathology


Assuntos
Feminino , Adulto , Humanos , Laparoscopia/métodos , Doenças Ovarianas/cirurgia , Diagnóstico Diferencial , Veias/fisiopatologia , Obstrução Uretral/etiologia
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